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DeCS

Descriptor English:

Caroli Disease

Descriptor Spanish:

enfermedad de Caroli

Descriptor Portuguese:

Doença de Caroli

Synonyms English:

Caroli Syndrome
Caroli's Disease
Caroli's Syndrome
Carolis Disease
Carolis Syndrome
Disease, Caroli
Disease, Caroli's
Syndrome, Caroli's

Tree Number:

Definition English:

Congenital cystic dilatation of the intrahepatic bile ducts (BILE DUCTS, INTRAHEPATIC). It consists of 2 types: simple Caroli disease is characterized by bile duct dilatation (ectasia) alone; and complex Caroli disease is characterized by bile duct dilatation with extensive hepatic fibrosis and portal hypertension (HYPERTENSION, PORTAL). Benign renal tubular ectasia is associated with both types of Caroli disease.

History Note English:

2004 (1993)

Allowable Qualifiers English:

Record Number:

30799

Unique Identifier:

D016767

Similar:

DeCS